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Syndromic X-Linked Intellectual Disability 17

Disease ID: disease_node_13619

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DbxrefMIM:300858, ORDO:289483
SubclassofDOID_0080012, DOID_0060309
Data SourceDOID
SynonymsX-linked mental retardation with alacrima and achalasia, intellectual disability-alacrima-achalasia syndrome, mental retardation, X-linked, syndromic 17
Doid Labelsyndromic X-linked intellectual disability 17
Doid DescriptionA syndromic X-linked intellectual disability characterized by global developmental delay, delayed motor development, lack of speech development, intellectual disability, alacrima and in some patients achalasia and/or anisocoria that has_material_basis_in variation in the chromosome region Xp21.1-p11.23.
Has Material Basis InGENO_0000149
Disease Node Iddisease_node_13619
Doid IdDOID_0060803
LabelSyndromic X-Linked Intellectual Disability 17