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Female-Restricted Syndromic X-Linked Intellectual Disability 99

Disease ID: disease_node_13596

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DbxrefGARD:13638, MIM:300968
SubclassofDOID_0060309, DOID_0080009
Data SourceDOID
SynonymsMRXS99F, X-linked female restricted facial dysmorphism-short stature-choanal atresia-intellectual disability, female-restricted syndromic X-linked mental retardation 99
Doid Labelfemale-restricted syndromic X-linked intellectual disability 99
Doid DescriptionA syndromic X-linked intellectual disability characterized by delayed psychomotor development, mild to moderate intellectual disability, and a wide range of additional congenital anomalies that has_material_basis_in heterozygous mutation in the USP9X gene on chromosome Xp11.4.
Has Material Basis InGENO_0000146
Disease Node Iddisease_node_13596
Doid IdDOID_0112025
LabelFemale-Restricted Syndromic X-Linked Intellectual Disability 99