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Deafness, Dystonia, And Cerebral Hypomyelination

Disease ID: disease_node_13588

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DbxrefGARD:12472, MIM:300475, ORDO:369939
SubclassofDOID_225, DOID_0080009
Data SourceDOID
Synonymssevere motor and intellectual disabilities-sensorineural deafness-dystonia syndrome, severe motor and intellectual disabilities-sensorineural hearing loss-dystonia syndrome
Doid Labeldeafness, dystonia, and cerebral hypomyelination
Doid DescriptionA syndrome characterized by motor and intellectual disabilities, dystonia, sensorineural deafness, white-matter changes and disorganization of the Golgi apparatus that has_material_basis_in heterozygous mutation in the BCAP31 gene on chromosome Xq28.
Has Material Basis InGENO_0000146
Disease Node Iddisease_node_13588
Doid IdDOID_0112123
LabelDeafness, Dystonia, And Cerebral Hypomyelination