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X-Linked Retinitis Pigmentosa And Sinorespiratory Infections

Disease ID: disease_node_13361

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DbxrefMIM:300455, ORDO:247522
SubclassofDOID_225, DOID_0050735
Data SourceDOID
Synonymsprimary ciliary dyskinesia-retinitis pigmentosa syndrome
Doid LabelX-linked retinitis pigmentosa and sinorespiratory infections
Doid DescriptionA syndrome characterized by retinitis pigmentosa and recurrent respiratory infections with nasal ciliary abnormalities and hearing loss in some patients that has_material_basis_in mutation in the RPGR gene on chromosome Xp11.4.
Has Material Basis InGENO_0000936
Disease Node Iddisease_node_13361
Doid IdDOID_0112124
LabelX-Linked Retinitis Pigmentosa And Sinorespiratory Infections