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Immunodeficiency 50

Disease ID: disease_node_13343

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DbxrefMIM:300988, ORDO:504530
SubclassofDOID_0080012, DOID_0111962
Data SourceDOID
SynonymsCID due to Moesin deficiency, IMD50, MSN-related combined immunodeficiency, X-linked Moesin-associated immunodeficiency, combined immunodeficiency due to Moesin deficiency, immunodeficiency 50 X linked recessive
Doid Labelimmunodeficiency 50
Doid DescriptionA combined immunodeficiency characterized by profound lymphopenia, hypogammaglobulinemia, poor immune response to vaccine antigens, fluctuating neutropenia and onset in early childhood of recurrent bacterial or varicella zoster virus infections that has_material_basis_in hemizygous mutation in MSN on chromosome Xq12.
Has Material Basis InGENO_0000149
Disease Node Iddisease_node_13343
Doid IdDOID_0112001
LabelImmunodeficiency 50