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X-Linked Immunodeficiency With Magnesium Defect, Epstein-Barr Virus Infection, And Neoplasia

Disease ID: disease_node_13308

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DbxrefMIM:300853
SubclassofDOID_0080012, DOID_628
Data SourceDOID
SynonymsXMEN
Doid LabelX-linked immunodeficiency with magnesium defect, Epstein-Barr virus infection, and neoplasia
Doid DescriptionA T cell deficiency that is characterized by CD4 lymphopenia, severe chronic viral infections, and defective T-lymphocyte activation in males and has_material_basis_in X-linked inheritance of mutations in the gene encoding magnesium transporter-1 (MAGT1).
Has Material Basis InGENO_0000149
Disease Node Iddisease_node_13308
Doid IdDOID_0080319
LabelX-Linked Immunodeficiency With Magnesium Defect, Epstein-Barr Virus Infection, And Neoplasia