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Immunodeficiency 70

Disease ID: disease_node_13306

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DbxrefMIM:618969
SubclassofDOID_0050736, DOID_628
Data SourceDOID
SynonymsIMD70
Doid Labelimmunodeficiency 70
Doid DescriptionA combined T cell and B cell immunodeficiency characterized by decreased CD4+ T cells, decreased CD19+ B cells, recurrent bacterial infections, and severe cutaneous warts on the hands, feet, and face that has_material_basis_in heterozygous mutation in the IVNS1ABP gene on chromosome 1q25.3.
Has Material Basis InGENO_0000147
Disease Node Iddisease_node_13306
Doid IdDOID_0112005
LabelImmunodeficiency 70