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Immunodeficiency 36

Disease ID: disease_node_13302

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DbxrefMIM:616005, NCI:C176703, UMLS_CUI:C4014934
SubclassofDOID_0050736, DOID_628
Data SourceDOID
SynonymsIMD36, activated phosphoinositide 3-kinase delta syndrome 2
Doid Labelimmunodeficiency 36
Doid DescriptionA combined T cell and B cell immunodeficiency characterized by recurrent respiratory tract infections, lymphoproliferation, and antibody deficiency that has_material_basis_in heterozygous mutation in the PIK3R1 gene on chromosome 5q13.1.
Has Material Basis InGENO_0000147
Disease Node Iddisease_node_13302
Doid IdDOID_0111949
LabelImmunodeficiency 36