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Immunodeficiency 15A

Disease ID: disease_node_13298

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DbxrefMIM:618204, UMLS_CUI:C4748694
SubclassofDOID_0050736, DOID_628
Data SourceDOID
SynonymsIMD15A
Doid Labelimmunodeficiency 15A
Doid DescriptionA combined T cell and B cell immunodeficiency characterized by immune dysregulation, combined T and B cell deficiency, inflammation, and epithelial defects that has_material_basis_in heterozygous missense mutation in the IKBKB gene on chromosome 8p11.21.
Has Material Basis InGENO_0000147
Disease Node Iddisease_node_13298
Doid IdDOID_0111960
LabelImmunodeficiency 15A