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Neonatal-Onset Type Ii Citrullinemia

Disease ID: disease_node_13243

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DbxrefMIM:605814
SubclassofDOID_0050737, DOID_9273
Data SourceDOID
Synonymsneonatal-onset type 2 citrullinemia
Doid Labelneonatal-onset type II citrullinemia
Doid DescriptionA citrullinemia that is characterized by confusion, restlessness, memory loss, abnormal behaviors (such as aggression, irritability, and hyperactivity), seizures and coma, caused by citrin deficiency (NICCD), and has_material_basis_in homozygous or compound heterozygous mutation in the SLC25A13 gene.
Has Material Basis InGENO_0000148
Disease Node Iddisease_node_13243
Doid IdDOID_0070341
LabelNeonatal-Onset Type Ii Citrullinemia