This website is for informational and educational purposes only. Please do not self-medicate; contact a medical professional for advice before administration. This website is for informational and educational purposes only. Please do not self-medicate; contact a medical professional for advice before administration.

Loeys-Dietz Syndrome

Disease ID: disease_node_12127

Connections displayed (default: 10).
Loading graph...

DbxrefGARD:10788, MESH:D055947, NCI:C75006, ORDO:60030, SNOMEDCT_US_2023_03_01:446263001, UMLS_CUI:C1836635, UMLS_CUI:C2697932
SubclassofDOID_0050736, DOID_225
Data SourceDOID, MESH
Mesh IdD055947
Mesh LabelLoeys-Dietz Syndrome
Mesh SubclassofD030342, D000015, D019465, D001014
Doid LabelLoeys-Dietz syndrome
Doid DescriptionA syndrome that is characterized by increased risk of aortic aneurysm and dissection, elongated limbs, hypertelorism, bifid uvula and easy skin bruising due to mutations in TGFB3 that results in connective tissue defects. Xref MGI. OMIM mapping confirmed by DO. [SN].
Has Material Basis InGENO_0000147
Disease Node Iddisease_node_12127
Doid IdDOID_0050466
LabelLoeys-Dietz Syndrome