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Neuroacanthocytosis

Disease ID: disease_node_11953

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DbxrefGARD:3956, MESH:D054546, MIM:200150, NCI:C84926, ORDO:2388, SNOMEDCT_US_2023_03_01:26848004, UMLS_CUI:C0393576
SubclassofDOID_0050737, DOID_0050765
Data SourceDOID, MESH
SynonymsLevine-Critchley syndrome, choreo-acanthocytosis
Mesh IdD054546
Mesh LabelNeuroacanthocytosis
Mesh SubclassofD002819, D020271
Doid Labelchoreaacanthocytosis
Doid DescriptionA neuroacanthocytosis characterized by progressive neurodegeneration and red cell acanthocytosis, with onset in the third to fifth decade of life and has_material_basis_in homozygous or compound heterozygous mutation in the VPS13A gene, which encodes chorein, on chromosome 9q21.
Has Material Basis InGENO_0000148
Disease Node Iddisease_node_11953
Doid IdDOID_0050766
LabelNeuroacanthocytosis