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Ichthyosis Bullosa Of Siemens

Disease ID: disease_node_11724

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DbxrefGARD:2966, MESH:D053560, MIM:146800, NCI:C84777, ORDO:455, SNOMEDCT_US_2023_03_01:254169002, UMLS_CUI:C0432306
SubclassofDOID_0050736, DOID_1697
Data SourceDOID, MESH
Synonymsbullous type ichthyosis, ichthyosis bullosa of Siemens, superficial epidermolytic ichthyosis
Mesh IdD053560
Mesh LabelIchthyosis Bullosa of Siemens
Mesh SubclassofD012873, D007057
Doid Labelbullous congenital ichthyosiform erythroderma
Doid DescriptionAn ichthyosis characterized by congenital erythema and widespread skin blistering, blisters develop into gray hyperkeratoses with a lichenified appearance, and that has_material_basis_in heterozygous mutation in the KRT2 gene on chromosome 12q13.
Has Material Basis InGENO_0000147
Disease Node Iddisease_node_11724
Doid IdDOID_0060877
LabelIchthyosis Bullosa Of Siemens