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Familial Hypophosphatemic Rickets

Disease ID: disease_node_11643

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DbxrefMESH:D053098, MIM:307800, NCI:C85234, UMLS_CUI:C0733682, UMLS_CUI:C1845168, UMLS_CUI:C3540852
SubclassofDOID_10609, DOID_0080009
Data SourceDOID, MESH
SynonymsHypophosphatemia, Vitamin D-Resistant Rickets, Vitamin D-Resistant Rickets, X-Linked, X-linked hypophosphatemia, hypophosphatemic rickets X-linked dominant
Mesh IdD053098
Mesh LabelFamilial Hypophosphatemic Rickets
Mesh SubclassofD007015, D063730
Doid LabelX-linked domit hypophosphatemic rickets
Doid DescriptionA rickets has_material_basis_in X-linked mutations in the PHEX gene that lead to increased circulating levels of FGF-23, a phosphate-regulating hormone (phosphatonin), that leads to reduced renal phosphate reabsorption and consequently abnormal bone mineralization. OMIM mapping confirmed by DO. [SN].
Has Material Basis InGENO_0000146
Disease Node Iddisease_node_11643
Doid IdDOID_0050445
LabelFamilial Hypophosphatemic Rickets