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Tay-Sachs Disease, Ab Variant

Disease ID: disease_node_11382

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DbxrefMESH:D049290, MIM:272750, NCI:C133084, SNOMEDCT_US_2023_03_01:71253000, UMLS_CUI:C0268275
SubclassofDOID_3321
Data SourceDOID, MESH
SynonymsTay-Sachs disease AB variant, Tay-Sachs disease, variant AB
Mesh IdD049290
Mesh LabelTay-Sachs Disease, AB Variant
Mesh SubclassofD020143
Doid LabelGM2 gangliosidosis, AB variant
Doid DescriptionA GM2 gangliosidosis that is characterized by normal hexosaminidase A (HEXA) and hexosaminidase B (HEXB) but the inability to form a functional GM2 activator complex. OMIM mapping confirmed by DO. [SN].
Disease Node Iddisease_node_11382
Doid IdDOID_4795
LabelTay-Sachs Disease, Ab Variant