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Beta-Mannosidosis

Disease ID: disease_node_11225

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DbxrefMESH:D044905, MIM:248510, NCI:C84596, SNOMEDCT_US_2023_03_01:238047006, UMLS_CUI:C4048196
SubclassofDOID_3211
Data SourceDOID, MESH
SynonymsBeta-D-mannosidosis, beta-mannosidase deficiency, lysosomal beta-mannosidase deficiency
Mesh IdD044905
Mesh Labelbeta-Mannosidosis
Mesh SubclassofD044904
Doid Labelbeta-mannosidosis
Doid DescriptionA lysosomal storage disease that has_material_basis_in deficiency of the beta-A-manosidase enzyme resulting in the disruption of N-linked glycoprotein oligosaccharide catabolism. OMIM mapping confirmed by DO. [SN].
Disease Node Iddisease_node_11225
Doid IdDOID_3633
LabelBeta-Mannosidosis