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Ornithine Carbamoyltransferase Deficiency Disease

Disease ID: disease_node_10144

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DbxrefGARD:8391, ICD10CM:E72.4, MESH:D020163, MIM:311250, NCI:C84957, SNOMEDCT_US_2023_03_01:80908008, UMLS_CUI:C0268542
SubclassofDOID_9267
Data SourceDOID, MESH
Synonymsdeficiency of citrulline phosphorylase, ornithine transcarbamylase deficiency
Mesh IdD020163
Mesh LabelOrnithine Carbamoyltransferase Deficiency Disease
Mesh SubclassofD040181, D056806
Doid Labelornithine carbamoyltransferase deficiency
Doid DescriptionAn urea cycle disorder that involves a mutated and ineffective form of the enzyme ornithine transcarbamylase. OMIM mapping confirmed by DO. [SN].
Disease Node Iddisease_node_10144
Doid IdDOID_9271
LabelOrnithine Carbamoyltransferase Deficiency Disease