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Alpha 1-Antitrypsin Deficiency

Disease ID: disease_node_10038

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DbxrefGARD:5784, ICD10CM:E88.01, ICD9CM:273.4, MESH:D019896, MIM:613490, NCI:C84397, SNOMEDCT_US_2023_03_01:30188007, UMLS_CUI:C0221757
SubclassofDOID_2345
Data SourceDOID, MESH
SynonymsAAT deficiency
Mesh IdD019896
Mesh Labelalpha 1-Antitrypsin Deficiency
Mesh SubclassofD008107, D013352, D008171, D030342
Doid Labelalpha 1-antitrypsin deficiency
Doid DescriptionA plasma protein metabolism disease that has_material_basis_in defective production of the protease inhibitor alpha 1-antitrypsin (A1AT), leading to decreased A1AT activity in the blood and lungs, and deposition of excessive abnormal A1AT protein in liver cells. OMIM mapping confirmed by DO. [SN].
Disease Node Iddisease_node_10038
Doid IdDOID_13372
LabelAlpha 1-Antitrypsin Deficiency